Late ventricular potentials in familial Mediterranean fever with and without AA amyloidosis
نویسندگان
چکیده
منابع مشابه
Late ventricular potentials in familial Mediterranean fever with and without AA amyloidosis.
Objective Familial Mediterranean fever (FMF) is an autosomal recessive disease characterized by episodic and chronic inflammation that may lead to both accelerated coronary atherosclerosis and cardiac AA amyloidosis. We hypothesized that late ventricular potentials (LPs), an established electrocardiographic susceptibility marker of ventricular arrhythmias, will be more common in FMF than in the...
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A 54-year-old Japanese man presented with recurrent abdominal pain, fever lasting >5 days, and renal failure. AA amyloidosis was proven by renal and gastric biopsy. Symptoms subsided with the administration of colchicine, but a subsequent recurrence of symptoms did not respond to colchicine. Mediterranean fever gene (MEFV) analysis showed that he was heterozygous for mutations in exon 2 (E148Q/...
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ژورنال
عنوان ژورنال: European Journal of Rheumatology
سال: 2017
ISSN: 2147-9720,2148-4279
DOI: 10.5152/eurjrheum.2017.16113